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CanVar-UK datasets

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CanVar-UK dataset summary

For selected genes, CanVar-UK presents data from the below functional assays, splicing assays and multifactorial genetic epidemiology studies. The applicable evidence strengths for assay readouts under the PS3 and BS3 ACMG criteria can be viewed here.

We aim to include key publications for selected genes, however this is not an exhaustive collection of all available datasets; to request the addition of a functional, splicing or genetic epidemiology dataset of interest, please email us at CanVIG@icr.ac.uk.

Functional datasets
Publication Year PMID # variants
ATM
Lee et al. 2025 40580951 29352
BAP1
Waters et al. 2024 38969833 7557
BARD1
Woo et al. 2025 41282735 6339
BRCA1
Dace et al. 2025 Preprint 3526
Bouwman et al. 2020 32546644 288
Fernandes et al. 2019 30765603 398
Petitalot et al. 2019 30257991 90
Findlay et al. 2018 30209399 3893
Starita et al. 2018 30219179 1093
Bouwman et al. 2013 23867111 86
BRCA2
Huang et al. 2025 39779857 6959
Sahu et al. 2025 39779848 6551
Hu et al. 2024 38417439 510
Hu et al. 2022 35736817 144
Richardson et al. 2021 33609447 275
Biswas et al. 2020 33293522 101
Ikegami et al. 2020 32444794 283
Hart et al. 2019 29884841 229
Mesman et al. 2019 29988080 43
Guidugli et al. 2018 29394989 139
CDKN2A
Kimura et al. 2025 40238651 1377
CHEK2
Gebbia et al. 2024 39642869 4878
McCarthy-Leo et al. 2024 39146382 4887
Stolarova et al. 2023 37449874 429
MLH1
Bouvet et al. 2019 30998989 44
Drost et al. 2019 30504929 38
Drost et al. 2010 20020535 26
MSH2
Jia et al. 2021 33357406 5872
Drost et al. 2019 30504929 35
Drost et al. 2012 22102614 25
Bouvet et al. 2019 30998989 44
MSH6
Drost et al. 2012 22102614 20
MUTYH
Hemker et al. 2025 40738107 4308
PALB2
Boonen et al. 2026 41554690 2539
PTEN
Matreyek et al. 2018 29785012 1965
Mighell, Evans-Dutson & O'Roak 2018 29706350 2786
RAD51C
Olvera-Leon et al. 2024 39299233 3849
RAD51D
Casadei et al. 2026 42327150 3273
STK11
Zimmerman et al. 2025 40791513 3888
TP53
Funk et al. 2025 39774325 1872
Kotler et al. 2018 29979965 1528
Giacomelli et al. 2018 30224644 8258
Kawaguchi et al. 2005 16007150 218
Kato et al. 2003 12826609 2320
TSC2
Biar et al. 2026 41648336 4279
VHL
Buckley et al. 2024 38969834 2268
Splicing assay datasets
Publication Year PMID # variants
BRCA1
Walker et al. 2013 23893897 252
Houdayer et al. 2012 22505045 113
BRCA2
Walker et al. 2013 23893897 194
Houdayer et al. 2012 22505045 159
Multiple genes
Wai et al. 2020 32123317 99
Wessex Clinical Genetics Service N/A N/A 112
Multifactorial genetic epidemiology studies
Publication Year PMID # variants
BRCA1
Caputo et al. 2021 34597585 40
Li et al. 2020 31853058 1302
Parsons et al. 2019 31131967 523
Vallée et al. 2012 21990165 113
Easton et al. 2007 17924331 105
BRCA2
Caputo et al. 2021 34597585 50
Li et al. 2020 31853058 2167
Parsons et al. 2019 31131967 872
Vallée et al. 2012 21990165 104
Easton et al. 2007 17924331 88